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    <subfield code="a">2186-361X</subfield>
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    <subfield code="a">Prashanth Prabhu</subfield>
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  <datafield tag="245" ind1=" " ind2="0">
    <subfield code="a">Audiological findings from an adult with thin cochlear nerves</subfield>
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  <datafield tag="260" ind1=" " ind2=" ">
    <subfield code="c">2017</subfield>
  </datafield>
  <datafield tag="270" ind1=" " ind2=" ">
    <subfield code="a">All India Institute of Speech and Hearing, Manasagangothri</subfield>
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  <datafield tag="300" ind1=" " ind2=" ">
    <subfield code="a">72-75</subfield>
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  <datafield tag="490" ind1=" " ind2=" ">
    <subfield code="v">Volume 6  Issue 1</subfield>
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  <datafield tag="520" ind1=" " ind2=" ">
    <subfield code="a">Reported here are audiological findings from an adult with thin cochlear nerves. Magnetic resonance imaging (MRI) revealed that he had a thinner cochlear nerve in the left ear than in the right ear. He had a higher degree of hearing loss in the left ear and poor speech recognition scores for both ears. He had normal middle ear and cochlear functioning. The auditory brainstem response and acoustic reflexes were absent, indicating a retrocochlear pathology. Long latency responses (LLR) revealed normal cortical functioning. Hence, implantation of an auditory brainstem implant might be an option, but the patient would need to be aware of its limitations. This case highlights the importance of MRI in evaluating congenital malformations of the cochlear nerve when audiological findings indicate a retrocochlear pathology.</subfield>
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  <datafield tag="700" ind1=" " ind2=" ">
    <subfield code="a">Jyothi Shivaswamy</subfield>
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  <datafield tag="773" ind1=" " ind2=" ">
    <subfield code="a">Intractable &amp; rare diseases research</subfield>
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  <datafield tag="856" ind1=" " ind2=" ">
    <subfield code="u">https://doi.org/10.5582/irdr.2016.01081</subfield>
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    <subfield code="c">FJAS</subfield>
    <subfield code="y">FJAS</subfield>
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    <subfield code="c">17931</subfield>
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